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AMBRAS SYNDROME & TREATMENT

Read about ambras syndrome medical facts: what is the definition of ambras syndrome, medical treatment & how to treat ambras syndrome, information about the causes, clinical features, and related ambras syndrome diseases.

Definition: What is "Ambras syndrome"?

AMBRAS SYNDROME

Ambras syndrome is a genetic condition characterized by excessive hair throughout the body. It is also known as "hypertrichosis lanuginosa", congenital hypertrichosis universalis & congenital hypertrichosis lanuginose. Ambras syndrome affects only one person in 1 billion people. Less than 40 cases of Ambras syndrome have been documented worldwide. This condition is said to have genetic component with family histories of Ambras syndrome being reported in relation to affected patients. In the 19th century, people suffering from Ambras syndrome perform in sideshow acts or circuses. People described as "wolfmen" or "werewolves" due to their excessive hair growth are most likely sufferers of Ambras syndrome.

Treatment: How to Treat "Ambras syndrome"?

There is no available treatment for Ambras syndrome other than depilation.

Causes

The first hairs made by an embryo's hair follicles inside the womb are called "lanugo hairs", which grow unpigmented, fine & long. However, when the embryo reaches 8 months gestation, lanugo hairs are normally shed off & replaced by fine vellus hair to prepare for birth. While a few lanugo hairs may survive after birth, these are usually shed shortly after. When a child is born with plenty or all of the lanugo hairs, this child looks like he or she is covered in light fur. This appearance & excessively long hair throughout the body will persist throughout life.

Clinical Features

Andras syndrome is present since birth & normally persists throughout life. Sufferers of this disease have all-over long, body hair growth that is non-pigmented. However, all affected hair is fully pigmented terminal hair. This condition is usually associated with teeth defects. Some patients with congenital hypertrichosis lanuginose develop hair in limited body parts, such as face, arms, torso & legs.

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